Prediction of pulmonary hypertension related to systemic sclerosis by an index based on simple clinical observations…
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Pulmonary arterial hypertension (PAH) is a severe, life-limiting complication of systemic sclerosis (SSc). Guidelines recommend early detection and…
The prevalence and characteristics of pulmonary hypertension in adults with sickle cell disease have not been clearly established…
The objectives of this study were to compare the survival of patients with ILD-associated PH (PH-ILD) or pulmonary arterial hypertension (PAH) and to…
Systemic sclerosis (ScS) is very heterogeneous in its clinical presentation and its therapeutic care is not codified. A better knowledge of the patients…
The aim of the study was to assess the prevalence and characteristics of vertebral fractures in a cohort of adult patients with GD1…
Gaucher disease (GD), the most prevalent inherited lysosomal storage disorder, is caused by deficient glucocerebrosidase activity. Type 1 GD (GD1), the…
To characterize the epidemiology, management and impact on quality of life and outcome of paediatric pulmonary arterial hypertension, excluding…
To describe the history of SSc-associated pulmonary arterial hypertension (SSc-PAH) in patients with New York Heart Association (NYHA) functional class…
The EVAPIL scale is a self-questionnaire aimed to assess tolerability of oral contraceptives (OC)…
